Vnitr Lek 2018, 64(10):961-965 | DOI: 10.36290/vnl.2018.134

Weber-Christian disease: a case report

Kristína Brázdilová1,*, Daniel Čierny1, Katarína Hrubišková1, Lukáš Plank2, Zdenko Killinger1, Juraj Payer1
1 V. interná klinika LF UK a UNB, Nemocnica Ružinov, Bratislava, Slovenská republika
2 Ústav patologickej anatómie JLF UK a UNM, Martin, Slovenská republika

Weber-Christian disease is a rare disease from the group of chronic fibrosing conditions characterized by inflammation of the adipose tissue - panniculitis and fibrosing with frequent systemic manifestations. Etiopathogenesis of the disease is not fully known, participation of autoimmune mechanisms is anticipated. Here, we report a case of a patient with this rare disease, diagnosed after a long and demanding diagnostic process, including repeated laparotomies. However, after immunosuppressive therapy, clinical and laboratory symptomatology improved rapidly as well as the patient's quality of life.

Keywords: panniculitis; sclerosing mesenteritis; Weber-Christian disease

Received: April 7, 2018; Accepted: May 16, 2018; Published: October 1, 2018  Show citation

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Brázdilová K, Čierny D, Hrubišková K, Plank L, Killinger Z, Payer J. Weber-Christian disease: a case report. Vnitr Lek. 2018;64(10):961-965. doi: 10.36290/vnl.2018.134.
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