Vnitr Lek 1993, 39(1):54-58

[A rare occurrence of familial idiopathic pulmonary fibrosis].

P Václavík: Kardiologická ambulance, I. interní oddĕlení NsP Prerov.

Klíčová slova: Child, Preschool; Female; Humans; Male; Middle Aged; Pulmonary Fibrosis, genetics,

The author describes rare familial incidence of idiopathic pulmonary fibrosis. The disease occurred and was the cause of death in all three children under five years--the patient's daughters. The patient contracted the disease at the age of 59 years. When modern treatment is used, the course of the disease is so far favourable. The author discusses aetiopathogenetic and hereditary aspects of idiopathic pulmonary fibrosis. He reminds of contemporary possibilities of diagnosis of this rare but very serious pulmonary disease.